Acute soft head syndrome in a teenager with sickle cell anemia: A case report

Simple item page
dc.contributor.authorNg'weina F. Magitta
dc.contributor.authorFrancisca B. Komanya
dc.contributor.authorBaraka O. Alphonce
dc.contributor.authorMbelwa D. Bitesigilwe
dc.contributor.authorEmmanuel M. Sindato
dc.contributor.authorJohn R. Meda
dc.date.accessioned2024-08-20T04:50:27Z
dc.date.available2024-08-20T04:50:27Z
dc.date.issued2023
dc.descriptionFull text. Available at https://doi.org/10.1002/ccr3.8174
dc.description.abstractASHS is a rare complication of SCD, invariably occurring near puberty with hitherto elusive pathogenic mechanisms. ASHS often resolves spontaneously on conservative management, however, lack of awareness in the context of limited access to brain imaging could pose diagnostic challenges resulting in inappropriate management and untoward outcome. We present a case of a teenager who presented with subtle symptoms for which the diagnosis of sickle cell anemia (SCA) was delayed until he developed ASHS. LTM was a 16 years old boy with a history of recurrent joints pain since the age of 6 years, with a family history of SCA, but had initial negative sickling test. He presented with episodes of multiple joints pain, unprovoked scalp and left orbital swelling, low-grade fever and mild headache without any evidence for bleeding diathesis. The diagnosis of SCA was confirmed by hemoglobin electrophoresis. Computed tomography (CT) scan of the head revealed subgaleal heamatoma (SGH) and intraorbital haematoma without intracranial hemorrhage (ICH). He was managed conservatively with analgesics and hydration together with antibiotics for associated sepsis with complete resolution of clinical symptoms within 2 weeks. This case represents a rare scenario for a relatively mild SCA phenotype presenting with ASHS whose diagnosis poses an enigma in the resource-limited contex. It is therefore, prudent to recognize ASHS to avoid judicious interventions which could potentially result in untoward clinical outcome.
dc.identifier.citationMagitta, N. W. F., Komanya, F. B., Alphonce, B. O., Bitesigilwe, M. D., Sindato, E. M., & Meda, J. R. (2023). Acute soft head syndrome in a teenager with sickle cell anemia: A case report. Clinical Case Reports, 11(11), e8174.
dc.identifier.doi10.1002/ccr3.8174
dc.identifier.otherDOI: 10.1002/ccr3.8174
dc.identifier.urihttps://repository.udom.ac.tz/handle/20.500.12661/4883
dc.publisherWiley
dc.relation.ispartofClinical Case Reports
dc.titleAcute soft head syndrome in a teenager with sickle cell anemia: A case report
dc.typeArticle
oaire.citation.issue11
oaire.citation.volume11
Files
Original bundle
Now showing 1 - 1 of 1
Thumbnail Image
Name:
Acute_soft_head_syndrome_in_a_teenager_with_sickle.pdf
Size:
1.09 MB
Format:
Adobe Portable Document Format
Download
License bundle
Now showing 1 - 1 of 1
No Thumbnail Available
Name:
license.txt
Size:
1.71 KB
Format:
Item-specific license agreed upon to submission
Description:
Download
Collections
Journal Articles